One of the most mysterious of brain diseases, Huntington’s chorea, is usually diagnosed between the ages of 35 to 45 years and for some time leads to neurological disorders, mental changes and mental retardation. The features and symptoms of the disease according to the portal MedikForum.ru.
Huntington’s chorea (can also be called Huntington’s disease) is a hereditary dysfunction of the brain, which inexorably progresses, and have different forms of progression. The gradual withering away of areas of the brain continues until death, the average duration of illness ranges from 10 to 25 years – by this time the volume of the brain can be reduced by a third. The death of nerve cells in Huntington’s chorea contributes to the psychological and neurological changes, with the earlier occurring Huntington’s chorea, the faster and more aggressive, it flows.
The term “chorea” is of Greek origin and means “dance”. This is due to the fact that the disease in humans, sudden, involuntary movements, most often hands and feet, resembling a dance. However, motor problems are only part of the clinical picture of chorea Huntington.
The signs of Huntington’s disease. Mental disorders, talking about the disease, can occur ten years before other typical signs of chorea Huntington. In addition, there is a sudden movement disorders that start with uncontrolled and excessive movements of the hands, feet or other body parts. Later appear grimaces, swallowing difficulties and speech disorders. At the last stage of the disease, there is more immobility and muscle rigidity. In the course of the disease there is a progressive decline of intellectual abilities.
In General, the symptoms of Huntington’s chorea can be divided into three groups:
Neurological and physical signs. Involuntary and uncontrolled movements chorea Huntington are quick, angular and repetitive. Initially, they resemble harmless tics – winking, distortion of the mouth and involuntary movements of the fingers. From these weak in his early twitching disease then worsens to the so-called Gorelnik of hyperkinesis in which uncontrolled movements affecting the entire body.
In addition, there is a wavering gait, resembling the gait of a drunk and often leading to falls. In the further course of the disease have problems with speech and swallowing due to the loss of control over muscles of the tongue and mouth.
Another physical symptom of Huntington’s chorea is a decrease in pain, which is found in many patients with this disease. This can lead to an increase in the number of accidents.
Behavioral disorders and psychological symptoms. In the case of chorea Huntington changes can cause ill almost cease to recognize their habitual environment. It can cause psychosis or depression, increased anxiety, aggressiveness.
The decline in intelligence. Initially, the disease manifests in the arising difficulties with concentration and forgetfulness. Gradually, the skills of learning, adaptation to environment and ability to reason logically weaken stronger and may lead to symptoms similar to dementia.
Juvenile form of Huntington chorea. About ten percent of cases the disease starts at an early age before the onset of the 20th anniversary. The juvenile form is characterized by a much more rapid progression of the disease and its symptoms differ from symptoms in adults. Instead of involuntary movement in young patients, in contrast, increasing stiffness of limbs due to significantly increased muscle tone. These conditions can last from several minutes to several hours, leading to increased immobility.
In addition, when the juvenile form of Huntington chorea the face is starting to look like a mask, ill lose the ability to control expression.